D efinition — A well-differentiated tumor of mesothelial cells. Clinical Features Epidemiology An uncommon neoplasm occurring in women between 20 and 50 years of age. Some but not all have evidence of asbestos exposure. You’re Reading a Preview Become a…
D efinition — A rare benign disease consisting of multiloculated mesothelial-lined cysts in the peritoneum. Also termed “multiloculated peritoneal cyst.” Clinical Features Epidemiology Rare. Reproductive-age women. History of a prior abdominal procedure or surgery is often noted. Controversy as to…
D efinition — A rare, predominantly intraabdominal tumor associated with a specific chromosomal translocation (t11;22)(p13:q12) that produces a fusion transcript EWS Clinical Features Epidemiology Extremely rare, particularly in women. Typically seen in children and young adults. Specific cell of origin…
D efinition — A rare, poorly differentiated embryonal neuroectodermal tumor sometimes associated with a teratoma that mimics the central type of primitive neuroectodermal tumor (PNET). Clinical Features Epidemiology Extremely rare in the ovary. Belongs in the Ewing's family of tumors…
D efinition — Ovarian involvement is a rare metastatic presentation of this tumor. Clinical Features Epidemiology Most common mesenchymal tumor of the gastrointestinal tract. Driven by oncogenic KIT or PDGFRA mutations. Most common is an in-frame mutation of exon 11…
D efinition — An uncommon spindled mesenchymal neoplasm of variable behavior with a NAB2-STAT6 fusion gene arising in the submesothelial mesenchyme. Clinical Features Epidemiology Uncommon; originally described in pleura, but now reported in multiple soft tissue sites including the pelvis.…
D efinition — A sex cord stromal tumor with annular tubules and features of both granulosa and Sertoli cell tumors. Clinical Features Epidemiology These are rare tumors, comprising about 6% of sex cord stromal tumors and less than 1% of…
D efinition — A malignant small cell ovarian tumor with features of pulmonary neuroendocrine carcinomas. Clinical Features Epidemiology Mean age of 48 years, which is over 20 years older than the small cell carcinoma of hypercalcemic type (SCCHT). Not associated…
D efinition — A malignant rhabdoid tumor associated with hypercalcemia and mutations and inactivation in the SMARCA4 gene. Clinical Features Epidemiology Presents between childhood and menopause, predominating in the late teens and early twenties. Rarely familial, but kindreds with mutations…
D efinition — Variant of sex cord–stromal tumor of the ovary. Clinical Features Epidemiology Uncommon; accounts for less than 2% of all sex cord–stromal tumors. Predominant in the second and third decades. You’re Reading a Preview Become a Clinical Tree…