Definition Nonneoplastic urothelium-lined polypoid mesenchymal proliferation Clinical features You’re Reading a Preview Become a Clinical Tree membership for Full access and enjoy Unlimited articles Become membership If you are a member. Log in here
Definition Retroperitoneal fibrosis encompasses a spectrum of inflammatory and fibrosing diseases involving the retroperitoneal structures. Etiology not clearly understood in 2/3 cases; hence, idiopathic retroperitoneal fibrosis (IRF) Some studies argue that IRF is part of the spectrum of IgG4-related disease.…
Definition Obstruction of the flow of urine from the renal pelvis to the proximal ureter due to partial or total blockage at the ureteropelvic junction that can be congential or acquired Can be caused by structural abnormality (intrinsic disorganization, extrinsic…
Definition A well-differentiated neuroendocrine neoplasm arising within the renal parenchyma Clinical features Epidemiology Rare tumor (fewer than 100 cases reported) Average age, 52 years (range, 27–78 years) No gender predilection May arise occasionally in a horseshoe kidney or renal teratoma…
Definition An extremely rare spindle cell tumor with rare epithelial differentiation and the characteristic translocation t(X;18)(p11.2;q11) Clinical features Epidemiology Wide age range (15–71 years), with a mean age of 39 years No sex predilection; male-to-female ratio, 1:1 You’re Reading a Preview…
Definition Encompasses a spectrum of biphasic tumors composed of variable amounts of epithelial and stromal components, ranging from predominantly cystic tumors (adult cystic nephroma, CN) to variably solid tumors (mixed epithelial and stromal tumor, MEST) Clinical features Epidemiology Adult patients…
Definition Lesions that arise from the specialized interstitial cells of the renal medulla, which are thought to play a role in renin release and blood pressure regulation Clinical features Epidemiology Found in up to 37%–50% in autopsies No sex predilection…
Definition A rare tumor differentiating toward specialized smooth muscle cells of the glomerular afferent arteriole in the juxtaglomerular apparatus; associated with renin production and hypertension Clinical features Epidemiology Rare tumor with fewer than 100 cases published Affects adolescents and young…
Definition Angiomyolipoma (AML) composed predominantly, at least 80%, of epithelioid cells Clinical features Epidemiology Eight percent of AMLs in surgical cohorts have an epithelioid component (10% or more of the tumor). Mean age, 50 (range 30–80) years Both genders are…
Definition A mesenchymal neoplasm composed of variable proportions of abnormal blood vessels, cells with smooth muscle features and adipose tissue; believed to be derived from perivascular epithelioid cells (PEC); hence, also named PECOMA Clinical features Epidemiology Angiomyolipoma (AML) accounts for…