Synonyms ■ Dermatomyositis ■ Idiopathic inflammatory myopathies ■ Idiopathic inflammatory dermatomyopathies Key features ■ Autoimmune connective tissue disease of uncertain etiology demonstrating a bimodal age distribution with both juvenile and adult forms ■ Clinical and laboratory signs of proximal extensor…
Evidence Levels: A Double-blind study B Clinical trial ≥ 20 subjects C Clinical trial < 20 subjects D Series ≥ 5 subjects E Anecdotal case reports Open full size image Systemic sclerosis (SSc), sometimes referred to as scleroderma, is a…
Evidence Levels: A Double-blind study B Clinical trial ≥ 20 subjects C Clinical trial < 20 subjects D Series ≥ 5 subjects E Anecdotal case reports Open full size image Raynaud phenomenon (RP) is characterized by intermittent peripheral vasoconstriction leading…
Evidence Levels: A Double-blind study B Clinical trial ≥ 20 subjects C Clinical trial < 20 subjects D Series ≥ 5 subjects E Anecdotal case reports Open full size image Eosinophilic fasciitis (EF), also known as Shulman syndrome , is…
Evidence Levels: A Double-blind study B Clinical trial ≥ 20 subjects C Clinical trial < 20 subjects D Series ≥ 5 subjects E Anecdotal case reports Open full size image Dermatomyositis (DM) is an idiopathic inflammatory myopathy characterized by cutaneous…
Key Points Classic dermatomyositis involves a proximal inflammatory myopathy with a characteristic cutaneous eruption. In patients with clinically amyopathic dermatomyositis, skin disease is the prominent feature. Pathognomonic cutaneous findings of dermatomyositis include the heliotrope eruption and Gottron’s papules. In dermatomyositis,…