Tag Sheri Jones Oguh

Pompe Disease

Risk Combined incidence (infantile vs. late-onset): 1:40,000. Infantile form has higher incidence in African-American and Chinese populations. Late-onset disease has a higher incidence in the Netherlands. Perioperative Risks Respiratory insufficiency Aspiration pneumonia Pulm edema Myocardial ischemia Worry About Respiratory insufficiency,…