Introduction Among rare thoracic tumors not described in previous chapters, two are the most common. Bronchogenic cysts are derived from abnormal budding of the ventricular diverticulum in the mediastinum or the lung. Lymphangiomas arise from the lymphatic system and develop…
Introduction Scimitar syndrome (SS) is a rare congenital anomaly characterized by a partial (usually the right lower lobe) or complete unilateral anomalous pulmonary venous drainage in association with ipsilateral lung hypoplasia. The anomaly, also known as pulmonary venolobar syndrome or…
Introduction Fetal hydrothorax is an intrathoracic effusion arising in the fetus, which may occur unilaterally or bilaterally, and may be primary or secondary. Disease Definition Fetal hydrothorax (also pleural effusion) is an intrathoracic effusion, which may occur unilaterally or bilaterally.…
Introduction Bronchopulmonary sequestration (BPS) is a solid lung lesion of nonfunctioning pulmonary tissue, a supernumerary lobe of the lung, which lacks connection to the tracheobronchial tree and receives its blood supply from an aberrant systemic feeding artery, originating commonly from…
Introduction Congenital cystic adenomatous malformations (CCAMs) of the lung represent the most common lung defect diagnosed prenatally. CCAMs are intrapulmonary lesions with a typical hyperechoic appearance on ultrasound (US), with or without cystic components. Both sides of the lung, both…