Category Gastrointestinal Imaging

Caroli Disease

KEY FACTS Terminology Caroli disease : Congenital, multifocal, segmental, saccular dilation of large intrahepatic bile ducts (IHBDs) Type V choledochal cyst (Todani classification) Caroli syndrome (more common variant): Cystic bile duct dilation plus hepatic fibrosis (± portal hypertension) You’re Reading…