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Risk Occurs in 1–3% of the pregnant population Perioperative Risks Increased maternal and fetal morbidity and mortality Protracted labor Arrested labor Uterine rupture Increased rate of cesarean section Increased rate of forceps- or vacuum-assisted delivery Worry About Increased need for…

Risk True CNH is exceedingly rare; the exact incidence is unknown. In pts with neurologic injury, it is most often associated with pulm dysfunction or shunting (aspiration, pneumonia, pulm edema, and baseline disease). Primarily seen in comatose pts. No association…

Risk Extremely rare; global estimate: 1:1,000,000 births Over 100 reported cases Perioperative Risks Airway obstruction Difficult mask ventilation and/or difficult intubation Increased ICP from craniosynostosis Coexisting congenital anomalies, especially cardiac Overview Manifestation: Craniosynostosis Polysyndactyly Cardiac defects Obesity Maxillary or mandibular…

Risk Male > female 9% of pts with recurrent syncope; history of falls Increased incidence with age, rarely below age 50 y Peripheral vascular disease Head and neck cancer Perioperative Risks Presence of CSS does not increase rate of mortality,…

Risk Rare (1:40,000 in Japan) Perioperative Risks Hypoglycemia triggered by fasting Massive rhabdomyolysis and cardiac arrest described following GA and succinylcholine. (The response may be confused with malignant hyperthermia.) No evidence that susceptibility to malignant hyperthermia is associated with the…

Risk About 5% of all primary cardiomyopathies. Idiopathic type is rare, and may be familial. 50% of pts with AL-type amyloidosis are affected. Endomyocardial fibrosis is endemic in Africa, Asia, and Central and South America. Perioperative Risk Diastolic dysfunction and…

Risk Exact incidence unknown Incidence in USA: About 1:3000 to 1:4000 live births Incidence higher in African-Americans compared to Caucasians Highest incidence in Haiti and parts of Africa Perioperative Risks CHF Arrhythmias; atrial and ventricular Pulm and systemic thromboembolism Worry…

Epidemiology Approximately a 1:1000 incidence per y, increasing with age. M:F incidence ratio: 2:1. Most common cause of heart failure; accounts for 40% of all cases. Perioperative Risks CHF exacerbation Hypotension Pulmonary edema Myocardial ischemia/infarction Acute renal failure Malignant arrhythmias/pacemaker…

Risk Relatively common inherited disorder; 0.2% or 1 in 500 Americans are affected. It is equally distributed between males and females and has no racial group predominance. The median age of clinical manifestation is 35 years, but it can manifest…

Risk Accounts for approximately ∼10,000 deaths and ∼46,000 hospitalizations per year in USA; idiopathic DCM is one of the primary indications for cardiac transplantation. Often ages ∼20–60 y old but can affect older and younger pts as well. African-Americans >…