Risk Prevalence of cLQTS: Approximately 1:5000 live births. Incidence of cLQTS: 1 in 10,000. 60–70% of those diagnosed are females. Males under 10 y of age have the highest mortality. Pts usually present in childhood with a cardiac event. Perioperative…
Risk Prevalence in USA: 13.1% in people >20 y. Prevalence highest among Hispanics. Cigarette smoking is a risk factor. Incidence highest among men ≥45 y and women ≥55 y. Htn is a risk factor. Low HDL (<40 mg/dL) is a…
Risk Extremely rare but described in a variety of populations True incidence and prevalence unknown Perioperative Risks Chronically untreated Htn Worry About Undiagnosed cerebrovascular, CV, and/or renal disease secondary to chronic Htn Worsening of hypokalemia with hyperventilation and nasogastric suctioning…
Risk Estimated 318,389 individuals living with leukemia or in remission in USA Estimated 54,270 new cases and 24,450 deaths of leukemia in 2015 Males >females ALL greater in children (median age of diagnosis 14 y) CML, CLL, and AML common…
Risk X-linked recessive disorder due to deficiency on the enzyme HGPRT, resulting in the buildup of uric acid Incidence ∼5.2 per million male births (where symptoms appear) Perioperative Risks Hyperuricemia and hyperuricosuria (gout) Airway problems secondary to scarification from self-mutilation…
Risk Myelomeningocele (25–50%) Congenital urologic anomalies (25–50%) Healthcare workers (3–17%) Atopic individuals (6–11%) General population (0–6%) Perioperative Risks Anaphylactic reaction leading to hypotension, bronchospasm, and CV collapse You’re Reading a Preview Become a Clinical Tree membership for Full access and…
Risk Prevalence estimated to be 1:20,000 Affects equally males and females Third most common familial myopathy after myotonic dystrophy and Duchenne muscular dystrophy Perioperative Risks No greater risk of malignant hyperthermia than normal population. Possible risk of acute rhabdomyolysis if…
Risk Unknown true incidence. Few studies of very specific regions outside USA report prevalence between 0.48 and 3.42 per million. 60–84% of LEMS patients have SCLC. LEMS mostly affects middle-aged adults, with rare occurrence in children. Perioperative Risks Increased risk…
Risk Incidence estimated at 1:40,000 live births (but milder cases go unrecognized). Slight female predilection (63%). Perioperative Risks Cervical spine instability and cardiopulmonary complications. Often occurs in association with other clinical syndromes (e.g., fetal alcohol, Goldenhar). Worry About Exacerbation of…
Risk Incidence in USA: 20 hospitalizations per 100,000 children Most commonly in pts <3 y of age Asian and Pacific Islanders have a higher rate, implying an unknown genetic effect Infants <6 mo and children >5 y have a higher…