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Risk More common than previously thought. Prevalence ranges from 1:7000–15,000. Occurrence is usually sporadic or maternally inherited. Perioperative Risks Metabolic acidosis Respiratory and cardiac insufficiency/failure Delayed emergence Worry About Respiratory failure following sedation. Consider aspiration risk. Metabolic acidosis. Hypotension during…
Case Synopsis A 9-month-old boy, American Society of Anesthesiologists (ASA) class II, is undergoing craniosynostosis repair with general anesthesia consisting of 2.5% sevoflurane with oxygen and fentanyl. He has an endotracheal tube in place and is positioned prone on a…