Physical Address
304 North Cardinal St.
Dorchester Center, MA 02124
Desmoplastic SMALL Round Cell Tumor
D efinition — A rare, predominantly intraabdominal tumor associated with a specific chromosomal translocation (t11;22)(p13:q12) that produces a fusion transcript EWS/WT1.
Clinical Features
Epidemiology
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Extremely rare, particularly in women.
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Typically seen in children and young adults.
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Specific cell of origin is unknown, but a primitive progenitor cell is suggested by some.
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