Orbital Imaging

Posterior ocular staphyloma

Imaging General imaging features Imaging studies show thinning of the sclera with focal bulge. May be unilateral or bilateral. Computed tomography features Computed tomography (CT) shows bulging of posterior aspect of the globe away from optic disc, usually on the…

Venous lymphatic malformation

Imaging Magnetic resonance imaging (MRI) has the unique ability to characterize hemorrhage using hemoglobin’s paramagnetic qualities and makes it ideally suited to evaluate VLM. MRI clearly demonstrates the internal structure of subacute and chronic hemorrhagic cysts based on paramagnetic qualities.…

Orbital venous varix

Key points Definition: Orbital venous varix (OVV) is a rare intraorbital vascular malformation composed of single or multiple venous channels that may enlarge intermittently with changes in venous pressure. Synonym: Orbital venous malformation. Classic clue: Patients present with enophthalmos or…

Cavernous sinus thrombosis

Key points Definition: Cavernous sinus thrombosis (CST) is a potentially life-threatening complication usually secondary to infection, commonly coming from nose, sinuses, ears, or teeth. Synonyms: Cavernous sinus thrombophlebitis, septic cavernous sinus thrombosis. Classic clue: Patient presents with recent-onset HA, photophobia,…

Carotid-cavernous fistula

Key points Definition: Carotid-cavernous fistula (CCF) is an abnormal connection between the carotid artery and/or its branches and the cavernous sinus (CS). Classic clue: Patient presents with an acute onset of Dandy’s triad with pulsatile proptosis, chemosis, and bruit accompanied…

Congenital anophthalmia

Key points Definition: Congenital anophthalmia (CA) is a rare malformation causing unilateral, or bilateral eye absence. Classic clue: Anophthalmia is discovered at delivery and frequently found by fetal ultrasound (US). Anophthalmia is the medical term for absence of eyes coming…

Congenital orbital teratoma

Key points Definition: Congenital orbital teratomas (COTs) are rare tumors. They are usually benign, complex masses with cystic and solid components containing a mixture of fat, calcium, and bone. Synonyms: Orbital teratomas, teratomas. Classic clue: Huge orbital mass containing cystic…

Persistent hyperplastic primary vitreous

Key points Definition: Pathologic entity caused by abnormal hypertrophy of the ocular hyaloid system. Classic clue: Child presenting at or soon after birth with leukocoria, micropthalmia, fluid-fluid level, no calcifications, and persistent Cloquet’s canal is virtually pathognomonic. In normal embryologic…

Coloboma

Key points Definition: A coloboma is caused by a rare congenital defect with failure of the embryonic intraocular fissure to fuse during the first trimester of fetal development resulting in an elongated or malformed globe. Colobomas may arise in any…

Rhabdomyosarcoma

Key points Definition: Rhabdomyosarcoma (RMS) is a relatively rare sarcoma, frequently found in children aged between 1 and 5 years. Classic clue: A 5-year-old old child is referred by a pediatrician with a history of possible recent trauma, developing rapid…