Congenital Heart Disease

Tricuspid Valve Anomalies

How many anatomically different kinds of malformation can befall the tricuspid valve? Our database suggests that the answer is at least 12 ( Table 13.1 ). TABLE 13.1 Anatomic Types of Tricuspid Malformation Tricuspid Valve Anomaly No. of Cases Percent…

Double-Outlet and Common-Outlet Right Atrium

Definition The morphologically right atrium (RA) opens into both the morphologically right ventricle (RV) and the morphologically left ventricle (LV) via two atrioventricular (AV) valves resulting in double-outlet right atrium (DORA), or via a common AV valve resulting in common-outlet…

Common Atrioventricular Canal

Acknowledgment I would like to thank Silvio Litovsky, M.D., for his great help in analyzing the data on which this chapter is based. Definition The anomaly known as common atrioventricular canal (or atrioventricular septal defect) is characterized anatomically by incomplete…

Juxtaposition of the Atrial Appendages

The anomaly now known as juxtaposition of the atrial appendages (JAA) was first described, to the best of our knowledge, by Thore in 1843 in an 11-day-old boy with left-sided JAA. Thore wrote that this neonate had “une anomalie du…

Interatrial Communications

How common are interatrial communications —mostly the theostium secundum type of atrial septal defect and ostium primum type of atrial septal defect ( Figs. 9.1 and 9.2 )? Is atrial septal defect (ASD) a common and therefore statistically important problem,…

Pulmonary Venous Anomalies

Totally Anomalous Pulmonary Venous Connection/Drainage Definition Totally anomalous pulmonary venous connection (TAPVC) is an anomaly in which none of the pulmonary veins connect normally with the morphologically left atrium (LA). TAPVC used to be known as total anomalous pulmonary venous…

Systemic Venous Anomalies

We shall begin the specific anomalies section with systemic venous malformations because this book is organized in a venoarterial or blood-flow sequence—segment by segment, alignment by alignment, and connection by connection. The first question we must endeavor to answer is,…

Segmental Anatomy

The segmental approach to the diagnosis of congenital heart disease is based on an understanding of the morphologic and segmental anatomy of the heart. The morphologic anatomy of the heart is summarized in Chapter 3 . The segmental anatomy of…